Kostmann syndrome

Definition / meaning of Kostmann syndrome

An inherited disorder in which there is a lower-than-normal number of neutrophils (a type of white blood cell that is important in fighting infections). Infants with the disorder get infections caused by bacteria, and are at an increased risk of acute myelogenous leukemia (AML) or myelodysplasia (a bone marrow disorder). Also called congenital neutropenia, genetic infantile agranulocytosis, infantile genetic agranulocytosis, Kostmann disease, and Kostmann neutropenia.

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Find More About 'Kostmann syndrome'

Source(s):

The Web site of the National Cancer Institute (http://www.cancer.gov/)

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