Meaning of adenoid cystic carcinoma: An uncommon gland cancer known for creeping along nerves and for returning many years after treatment.

Definition of adenoid cystic carcinoma

Adenoid cystic carcinoma is an uncommon cancer that begins in glands which produce secretions, most often the salivary glands of the mouth and throat. It also arises in tear glands, the windpipe, the breast and the skin. It grows slowly but tends to travel along nerves, which makes complete removal difficult and allows it to return long afterward.

Where does it start?

Any tissue with secreting glands can give rise to it, though some sites are far more common than others.

SiteHow it usually shows itself
Salivary glandsA slow-growing lump in the mouth, jaw or neck
Tear glandA bulging eye or altered vision
Windpipe or airwayBreathlessness or a persistent cough
BreastA lump, often behaving less aggressively here

Why does it come back so late?

This carcinoma spreads by following the sheaths that wrap nerves, a pattern called perineural invasion. Tumor cells creep along these paths well beyond the lump a surgeon can see or feel, so margins that look clear may not be. That habit explains both the pain or numbness that can accompany it and the recurrences that appear a decade or more after apparently successful treatment. Long follow-up is the norm for this reason.

How is it different from other salivary gland cancers?

Most salivary tumors are benign. Among the malignant ones, mucoepidermoid carcinoma is more common and tends to declare itself sooner. Adenoid cystic carcinoma is set apart by three things: its slow pace, its attraction to nerves, and its tendency to reach the lungs rather than the surrounding lymph nodes. Under the microscope its cells form a distinctive pattern of small holes that has been likened to a slice of Swiss cheese.

Also known as

ACC

Used in a sentence

The pathology report described adenoid cystic carcinoma of the submandibular gland with perineural invasion.

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Good to know

Its spread along nerve sheaths means the tumor often extends past what can be seen at surgery, and recurrence more than ten years later is well recognized.

Word origin

Where “adenoid cystic carcinoma” comes from

Adenoid combines the Greek aden, meaning gland, with eidos, meaning form; carcinoma derives from the Greek karkinos, meaning crab.

For learning, not diagnosis. This glossary provides general educational information and is not a substitute for advice from a qualified healthcare professional. If you may be experiencing a medical emergency, contact local emergency services.